![]() ![]() The left globe was also small with left optic nerve atrophy. No nerve was visualized in the bilateral posteroinferior canals s/o vestibulocochlear nerve aplasia. MRI (3D DRIVE) axial plane revealed abnormal elongated cisternal segment of the facial nerve bilaterally. The anterosuperior canal continued with the facial nerve canal and the posteroinferior canal lead to the cochlear aperture and vestibule. 3) showed two narrow canals with separate course in the temporal bone. HRCT axial sections and coronal oblique reformatted images of case three (Fig. No nerve is visualized in the right posteroinferior canal s/o right eighth nerve aplasia ( arrows in f) Thin T2 hypointense nerve like structure is seen in the left posteroinferior canal reaching up to the modiolus s/o left cochlear nerve hypoplasia. ![]() MRI (3D DRIVE) axial plane ( e, f) reveal facial nerve in the bilateral anterosuperior canals ( arrows in e). The IAC is normal in orientation and overall size however the two canals are narrow in calibre. Coronal oblique reconstructed images ( c, d) better depict the complete partition. HRCT axial sections ( a, b) reveal the presence of two bony canals in the region of the IAC. The patient has undergone successful left cochlear implantation.Ĭase 2 Complete Partition Anomaly of the IAC. The patient was diagnosed as a case of bilateral complete partition anomaly of the internal auditory canal with aplasia of both lateral SCC with left cochlear nerve hypoplasia and right vestibulocochlear nerve aplasia. Thin T2 hypointense nerve like structure was seen in the left posteroinferior canal reaching up to the modiolus suggestive of hypoplastic left cochlear nerve and no nerve was visualized in the right posteroinferior canal s/o right eighth nerve aplasia. The facial nerve was identified in the bilateral anterosuperior canals on MRI (3D DRIVE sequence). Bilateral lateral semicircular canals (SCC) were aplastic. There were two narrow separate canals on both sides however, the IAC was normal in orientation and overall size. 2) HRCT revealed the presence of two bony canals in the region of the IAC with a complete partition bilaterally. HRCT temporal bone axial image ( c) at the level of inner ear shows the presence of two cystic rudimentary structures ( black arrows) in the location of cochlea and vestibule on both sides suggestive of incomplete partition type cystic cochleo-vestibular dysplasia Note that IAC is normal in orientation and overall size. HRCT axial sections ( a, b) superior to inferior reveal an incomplete bony septum ( arrow) dividing the IAC into two bony canals. These findings were suggestive of incomplete partition of the left internal auditory canal with bilateral cystic cochlea-vestibular dysplasia or incomplete partition type I deformity.Ĭase 1 Incomplete Partition Anomaly of the IAC. In addition there were two cystic rudimentary structures in the location of cochlea and vestibule bilaterally. However, the IAC was normal in orientation and overall size. 1) revealed an incomplete bony septum dividing the left IAC into two bony canals. High resolution CT (HRCT) axial sections temporal bone of case 1 (Fig. There was no significant family history of congenital disease or past history of medical illness. All three children had normal facial nerve function and no vestibular symptoms. The third patient also had left microphthalmos in addition to the hearing abnormality. Three children (4-year-old-boy, 6-year-old boy and 14-month-old boy respectively) with bilateral sensorineural hearing loss presented to our department for pre-operative imaging for cochlear implantation. ![]()
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